Pulmonary fibrosis indicative of granulomatosis with polyangiitis initially believed to be sjögren’s syndrome
نویسندگان
چکیده
منابع مشابه
An Unusual Presentation of Granulomatosis with Polyangiitis
The granulomatosis with polyangiitis (GPA), formerly known as Wegener’s granulomatosis, is a pauci-immune vasculitis involving small- and medium-sized blood vessels. Classically, the patients inflicted with this disease present with a triad of necrotizing granulomatous inflammation of the respiratory tract, cutaneous necrotizing vasculitis, and glomerulonephritis (GN). The antinuclear (ANA) and...
متن کاملGranulomatosis with polyangiitis initially misdiagnosed as lung cancer.
Granulomatosis with Polyangiitis (GPA), which was formerly named Wegener's Granulomatosis (WG) is a systemic disease characterized by necrotizing granulomatous inflammation and vasculitis that primarily involves upper and lower respiratory tract, as well as kidneys. Diagnosing GPA on the basis of transthoracic fine needle aspiration (TFNA) may be problematic, as it can be misdiagnosed as cancer...
متن کاملPulmonary manifestations of granulomatosis with polyangiitis.
OBJECTIVE To describe the clinical and laboratory data, with special emphasis on thoracic imaging findings, in 14 patients with a definitive diagnosis of granulomatosis with polyangiitis (GPA). METHODS The clinical and tomographic data of 14 patients with a definitive diagnosis of GPA are presented. Patients with thoracic manifestations suggestive of GPA were evaluated in 3 hospitals from 200...
متن کاملGranulomatosis With Polyangiitis (Wegener’s)
To determine outcomes in relation to duration of maintenance therapy in patients with granulomatosis with polyangiitis (Wegener’s) (GPA), we conducted a retrospective chart review of patients with GPA seen at a single vasculitis center from 1992 to 2010. All patients achieved remission defined by a Birmingham Vasculitis Activity Score for Wegener Granulomatosis (BVAS/WG) of 0 with either cyclop...
متن کاملChurg–Strauss syndrome (eosinophilic granulomatosis with polyangiitis): A case report
Churg–Strauss syndrome (CSS) is a rare systemic vasculitis of the small and medium sized blood vessels. The triad of asthma, sinusitis and hypereosinophilia is characteristic of CSS. However, it can affect any organ system with predominance for the skin, respiratory, neurological, gastrointestinal and cardiovascular systems. The natural history of the condition has been described in three phase...
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ژورنال
عنوان ژورنال: Internal Medicine Inside
سال: 2014
ISSN: 2052-6954
DOI: 10.7243/2052-6954-2-6